GALNS purified MaxPab rabbit polyclonal antibody (D01P)
产品名称： GALNS purified MaxPab rabbit polyclonal antibody (D01P)
英文名称： GALNS purified MaxPab rabbit polyclonal antibody (D01P)
产品编号： H00002588-D01P
产品价格： null
产品产地： 台湾
品牌商标： Abnova
更新时间： null
使用范围：
亚诺法生技股份有限公司（Abnova)
- 联系人 :
- 地址 : 台湾台北市内湖区洲子街 108 号 9 楼
- 邮编 : 11493
- 所在区域 : 台湾
- 电话 : +886-920**1152 点击查看
- 传真 : 点击查看
- 邮箱 : sales@abnova.com.tw
- Specification
- Product Description:
- Rabbit polyclonal antibody raised against a full-length human GALNS protein.
- Immunogen:
- GALNS (NP_000503.1, 1 a.a. ~ 522 a.a) full-length human protein.
- Sequence:
- MAAVVAATRWWQLLLVLSAAGMGASGAPQPPNILLLLMDDMGWGDLGVYGEPSRETPNLDRMAAEGLLFPNFYSANPLCSPSRAALLTGRLPIRNGFYTTNAHARNAYTPQEIVGGIPDSEQLLPELLKKAGYVSKIVGKWHLGHRPQFHPLKHGFDEWFGSPNCHFGPYDNKARPNIPVYRDWEMVGRYYEEFPINLKTGEANLTQIYLQEALDFIKRQARHHPFFLYWAVDATHAPVYASKPFLGTSQRGRYGDAVREIDDSIGKILELLQDLHVADNTFVFFTSDNGAALISAPEQGGSNGPFLCGKQTTFEGGMREPALAWWPGHVTAGQVSHQLGSIMDLFTTSLALAGLTPPSDRAIDGLNLLPTLLQGRLMDRPIFYYRGDTLMAATLGQHKAHFWTWTNSWENFRQGIDFCPGQNVSGVTTHNLEDHTKLPLIFHLGRDPGERFPLSFASAEYQEALSRITSVVQQHQEALVPAQPQLNVCNWAVMNWAPPGCEKLGKCLTPPESIPKKCLWSH
- Host:
- Rabbit
- Reactivity:
- Human
- Storage Buffer:
- In 1x PBS, pH 7.2
- Storage Instruction:
- Store at -20°C or lower. Aliquot to avoid repeated freezing and thawing.
- Quality Control Testing:
- Antibody reactive against mammalian transfected lysate.
- MSDS:
Download
- Applications
- Western Blot (Tissue lysate)
- GALNS MaxPab rabbit polyclonal antibody. Western Blot analysis of GALNS expression in human pancreas.
- Protocol Download
- Western Blot (Transfected lysate)
- Western Blot analysis of GALNS expression in transfected 293T cell line (H00002588-T01) by GALNS MaxPab polyclonal antibody.
Lane 1: GALNS transfected lysate(58.00 KDa).
Lane 2: Non-transfected lysate. - Protocol Download
- Entrez GeneID:
- 2588
- GeneBank Accession#:
- NM_000512.3
- Protein Accession#:
- NP_000503.1
- Gene Name:
- GALNS
- Gene Alias:
- FLJ17434,FLJ42844,FLJ98217,GALNAC6S,GAS,MPS4A
- Gene Description:
- galactosamine (N-acetyl)-6-sulfate sulfatase
- Omim ID:
- 253000
- Gene Ontology:
- Hyperlink
- Gene Summary:
- This gene encodes N-acetylgalactosamine-6-sulfatase which is a lysosomal exohydrolase required for the degradation of the glycosaminoglycans, keratan sulfate, and chondroitin 6-sulfate. Sequence alterations including point, missense and nonsense mutations, as well as those that affect splicing, result in a deficiency of this enzyme. Deficiencies of this enzyme lead to Morquio A syndrome, a lysosomal storage disorder. [provided by RefSeq
- Other Designations:
- chondroitinase
- Related Disease